• The principal cause of mortality is colorcctal canccr
• Patientś with untreated FAP have a median life expectancy of 42 years.
* Life cxpcctancy is cslcnded greatły in thosc treated with colcctomv.
* Uppcrgastrointcstinal canccrs and desmoidś arc tlić most common causes of death in patients who havc undergone colecłomy.
The cumuiatise probability of geyeloping any type of a noncolorectal canccr, mostly pcriampullars tumors, is 117. bv age 50 years and 52% by 75 years.